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1 ?婴儿型多囊肾(Infantile Polycystic Kidney Disease) 常染色体隐性遗传性多囊肾论文写作要点 somal reces-sive polycystic kidney disease,ARPKD),以往多称为婴儿型多囊肾病(infantile polycystic kidney disease,IPKD),是一种少见的肾脏和肝内胆管的遗传性畸形 阅读病例 6. 多囊肾病178例的遗传家系调查 [作 2 ?婴儿型多囊肾病 ...要点 somal reces-sive polycystic kidney disease,ARPKD),以往多称为婴儿型多囊肾病(infantile polycystic kidney disease,IPKD),是一种少见的肾脏和肝内胆管的遗传性畸形 阅读病例 6. 3 ?故又称小儿多囊肾病 ...种儿童肾脏及肝脏相关的严重的遗传病, 患者均婴幼儿时期起病,故又称小儿多囊肾病(infantilepolycystic kidneydisease,IPKD),发病率为1:20,000~1:40,000[H】。 4 ?以往多称为婴儿型多囊肾病 ...要点 somal reces-sive polycystic kidney disease,ARPKD),以往多称为婴儿型多囊肾病(infantile polycystic kidney disease,IPKD),是一种少见的肾脏和肝内胆管的遗传性畸形 阅读病例 6.
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