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单词 Congenital hepatic fibrosis
释义

Congenital hepatic fibrosis

英语百科

Congenital hepatic fibrosis

Congenital hepatic fibrosis has an autosomal recessive pattern of inheritance.

Congenital hepatic fibrosis is an inherited fibrocystic liver disease associated with proliferation of interlobular bile ducts within the portal areas and fibrosis that do not alter hepatic lobular architecture. The fibrosis would affect resistance in portal veins leading to portal hypertension.

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