Sodium phenylbutyrate

Nitrogen elimination by phenylbutyrate metabolites

Sodium phenylbutyrate is a salt of an aromatic fatty acid, 4-phenylbutyrate (4-PBA) or 4-phenylbutyric acid. The compound is used to treat urea cycle disorders, because its metabolites offer an alternative pathway to the urea cycle to allow excretion of excess nitrogen. It is an orphan drug, marketed by Ucyclyd Pharma under the trade name Buphenyl, by Swedish Orphan International (Sweden) as Ammonaps, and by Fyrlklövern Scandinavia as triButyrate.

单词	Buphenyl
释义	Buphenyl 英语百科 Sodium phenylbutyrate Sodium phenylbutyrate is a salt of an aromatic fatty acid, 4-phenylbutyrate (4-PBA) or 4-phenylbutyric acid. The compound is used to treat urea cycle disorders, because its metabolites offer an alternative pathway to the urea cycle to allow excretion of excess nitrogen. It is an orphan drug, marketed by Ucyclyd Pharma under the trade name Buphenyl, by Swedish Orphan International (Sweden) as Ammonaps, and by Fyrlklövern Scandinavia as triButyrate.
随便看	blandishment blandishments blanditude bland line bland liquid diet Blandlube blandly blandn bland necrosis blandness bland blandness of fats blando Blandon blandongan bland out Bland R. bland run blandscapes blandum Blandus bland valley Bland White Garland Bland White Garland syndrome Blandy