Congestive heart failure remains the greatest cause of death in primary amyloidosis due to the development of a rapidly progressive amyloidcardiomyopathy.
因为快速进展心肌淀粉样变,充血性心衰仍然是原发性淀粉样变的主要的死因。
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Amyloidcardiomyopathy is largely unresponsive to current heart failure therapies and is associated with a median survival of less than 6 months and a 5-year survival of less than 10%.